NCBI Accession #
NP_176198.1
NCBI GenBank Nucleotide #
NM_104682.3
NCBI Official Full Name
pyruvate dehydrogenase complex E1 alpha subunit
NCBI Official Symbol
E1 ALPHA
NCBI Official Synonym Symbols
AT-E1 ALPHA; pyruvate dehydrogenase complex E1 alpha subunit; PYRUVATE DEHYDROGENASE E1 ALPHA SUBUNIT
NCBI Protein Information
pyruvate dehydrogenase complex E1 alpha subunit
NCBI Summary
encodes the e1 alpha subunit of the pyruvate dehydrogenase complex (PDC)
UniProt Gene Name
E1 ALPHA
UniProt Synonym Gene Names
PDHE1-A
UniProt Protein Name
Pyruvate dehydrogenase E1 component subunit alpha-1, mitochondrial
UniProt Primary Accession #
P52901
UniProt Secondary Accession #
Q9C5E3; Q9SXC2
UniProt Related Accession #
P52901
UniProt Comments
The pyruvate dehydrogenase complex catalyzes the overall conversion of pyruvate to acetyl-CoA and CO2. It contains multiple copies of three enzymatic components: pyruvate dehydrogenase (E1), dihydrolipoamide acetyltransferase (E2) and lipoamide dehydrogenase (E3).